KMID : 1197720190120010027
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´ëÇÑÆÄŲ½¼º´ ¹× ÀÌ»ó¿îµ¿Áúȯ ÇÐȸÁö 2019 Volume.12 No. 1 p.27 ~ p.30
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The ¡®Hot Cross Bun¡¯ Sign Is Not Always Multiple System Atrophy: Etiologies of 11 Cases
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Way Christopher
Pettersson David Hiller Amie
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Abstract
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Objective: To clarify the specificity of the ¡®hot cross bun¡¯ sign (HCBS) for multiple system atrophy (MSA) in adult cerebellar ataxia or parkinsonism.
Methods: The radiologic information systems at an academic center and affiliated veterans¡¯ hospital were queried using the keywords ¡®hot cross bun,¡¯ ¡®pontocerebellar,¡¯ ¡®cruciate,¡¯ ¡®cruciform,¡¯ ¡®MSA,¡¯ ¡®multiple system atrophy,¡¯ and ¡®multisystem atrophy.¡¯ Scans were reviewed by a neurologist and neuroradiologist to identify the HCBS. Subjects with the HCBS were reviewed by 2 neurologists to identify the most likely etiology of the patient¡¯s neurologic symptoms.
Results: Eleven cases were identified. Etiologies included MSA (4 probable, 2 possible), hereditary cerebellar ataxia (3/11), probable dementia with Lewy bodies (1/11), and uncertain despite autopsy (1/11).
Conclusion: MSA was the most common etiology. However, 5 of the 11 patients did not have MSA. The most common alternate etiology was an undefined hereditary cerebellar ataxia (3/11).
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KEYWORD
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Multiple system atrophy, olivopontocerebellar atrophy, magnetic resonance imaging, cerebellar ataxia
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